A rare childhood uterine malignancy combined with complete uterine inversion

Česká verzia

Authors: Lucie Klenovská ¹ ; Ivana Meixnerová ¹ ; Luboš Minář ¹ ; Marta Ježová ²
Authors place of work: Gynekologicko-porodnická klinika LF MU a FN Brno ¹; Ústav patologie, LF MU a FN Brno ²
Published in the journal: Ceska Gynekol 2025; 90(3): 231-237
Category:
doi: https://doi.org/10.48095/cccg2025231

Summary

Objective: An overview of the types of uterine sarcoma, supplemented by an illustrative case report of a rare uterine childhood tumor. Case report: Our case report describes the case of a 9-year-old girl with a 15-cm tumor in the abdominal cavity, which prolapsed vaginally before introitus during a clinical examination of the abdominal wall causing life-threatening bleeding. This bleeding was stopped by ligation of the tumor pedicle and its resection. Histological examination of the resected specimen described Müllerian adenosarcoma of the uterus. Based on the staging, laparoscopic hysterectomy with bilateral salpingectomy was indicated by the oncogynecological committee. The operation was performed without complications, and intraoperatively, a complete inversion of the uterus was diagnosed.

Keywords:

Leiomyosarcoma – uterine inversion – uterine sarcoma – endometrial stromal sarcoma – Müllerian adenosarcoma

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ORCID autorů

L. Klenovská 0009-0003-2297-9627

I. Meixnerová 0000-0002-4837-4795

L. Minář 0000-0001-9088-5428

Doručeno/Submitted: 4. 12. 2024

Přijato/Accepted: 12. 12. 2024

doc. MUDr. Luboš Minář, Ph.D.

Gynekologicko-porodnická klinika

LF MU a FN Brno

Obilní trh 526/11